medigraphic.com

2014, Number 2

Rev Cubana Pediatr 2014; 86 (2)

Peutz-Jeghers syndrome as a cause of intestinal intussusception in the child

Vázquez ME, Vialat SV, Vázquez MYE, Vázquez MYT

Language: Español
References: 20
Page: 245-251
PDF size: 116.00 Kb.


ABSTRACT

Intestinal intussusceptions is a frequent cause of occlusive syndrome in breastfeeding and ileocolic intussusceptions is the most frequent one, but jejuno-jejunal intussusceptions has low incidence at pediatric ages. It is said that over 50 % of cases are seen in children older than 10 years and generally secondary to intestinal polyps, more frequently with Peutz-Jeghers syndrome. They are hamartomatosus, potentially malignant polyps, hence, these patients should be strictly followed-up. This is the case of a 13 years-old boy, with a history of this type of syndrome, who was admitted to the hospital because on colic-type abdominal pain and vomiting. Simple abdominal X-ray showed pattern of intestinal occlusion. Abdominal echography with target images indicated intestinal intussusception. The patient was operated on and underwent intestinal resection and termino-terminal anastomosis due to existing intestinal polyp in the jejunum. He recovered satisfactorily. A literature review was made on this infrequent ailment.

References

  1. Colombani PM, Scholz S. Intussusception. In: Coran AG. Pediatric Surgery. 7 ed. Philadelphia: Saunders; 2011. p. 1093-110.

  2. Fallat ME. Intussusception. In: Ashcraft KW. Pediatric Surgery. 3 ed. Philadelphia: Saunders; 2000. p. 518-26.

  3. Quian J, Mas M, Jurado R. Invaginación Intestinal. Estudio de su incidencia un año en Uruguay. Arch Pediatr Urug. 2005;76(2)110-7.

  4. Osamu Doi AM, Kofi Aoyama AG, Huntson JM. Twenty one cases of small bowel intussusception: the pathology of idiopatic intussusception and the concept of benign small bowel intussusceptions. Pediatr Surgery Int. 2004;20:135-43.

  5. Barussaud M, Regenet N, Briennon X. Clinical spectrum and surgical approach of adult intussusceptions: a multicentric study. Int J Colorectal Dis. 2005;11:32-6.

  6. Peutz JLA. On a vary remarkable case of familial polyposis of mucomembrane of intestinal tract and nosopharynx accompanied by peculiar pigmentation of skin a mucous membrane. Ned M G. 1921;10:134-46.

  7. Hutson JM, O'Brien M, Woodward AA, Beasley SW. Intussusception. In: Jones' Clinical Paediatric Surgery. Diagnosis and Management. Sixth edition. Melbourne: Blackwell Publishing; 2008. p. 126-32.

  8. Olch Wang S, Maike D, Sel S. Peutz-Jeghers disease: most but not all, families are compatible with linkage to 19p 13.3. J MED Genet. 1998;35:42-6.

  9. Giardello FM, Bunsinger JD, Tersmette AC. Very high risk of cancer in familial Peutz-Jeghers syndrome. Gastroenterology. 2000;119:1447.

  10. Van Tier MG, Wagner A, Mathus- Vliegen EM. High cancer risk in Peutz-Jeghers syndrome: a systematic review and surveillance recommendations. Am J Gastroenterology. 2010;105:1230-58.

  11. Cunninghan JD, Vine AJ, Karrch L. The role of laparoscopy in the management of intussusceptions in the Peutz-Jeghers syndrome: case report and review of the literature. Laparosc Endosc Percutan Techn. 1998;8:17.

  12. Hinds R, Philp C, Hyer W. Fell JM. Complications of childhood Peutz-Jeghers syndrome implication for pediatric screening. J Pediatric Gastroenterol Nutr. 2004;39:219-30.

  13. Edwards DP, Khosva VK, Staffer T, Phillips RK. Long term results of polypo clearance by intraoperative enteroscopy in the Peutz-Jeghers Syndrome. Dis Recto M. 2003;46:48-60.

  14. Navarro O, Daneman A. Intussusception. Diagnosis and management of those that reduce spontaneously. Ped Radiol. 2004;34:305-12.

  15. Muden M, Fruzzi J, Coley B, Minden R. Sonography of pediatric small bowell intussusceptions: differentiation from no surgical cases. AJR. Jan 2007;188:275-9.

  16. Koplewitz B, Simanousky N, Lensart P, Udassin R, Abu-Dalm K, Arbell D. Air encircling the intussusceptions on air enema for intussusceptions reduction and indication for surgery? Br J of Radiology. 2011;84:719-26.

  17. Georgeson KE. Laparoscopic management of ileocolic intussusceptions. In: George W. Holcomb III. Atlas of pediatric laparoscopy and thoracoscopy. Philadelphia: Saunders Elsevier; 2008. p. 71-5.

  18. Kaiser AD, Applegate KE, Ladd AP. Current in the treatment of the intussusceptions in children. J Surg. 2007;10:469-74.

  19. Boychuk RB, Franke AA. Intussusception. AM Journal of Emerg Medicine. 2011;29:353-5.

  20. Simanousky N, Hiller N, Koplewitz B, Eliahou R, Udassin R. In: No-operative intussusception reduction effective in older children? Ten year experience in a university affiliated Medical Center. Pediatr Surg Int. 2007;23:261-4.

2020     |     www.medigraphic.com