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2014, Number 2

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Mediciego 2014; 20 (2)

Prune-Belly Syndrome. A case presentation

Portela RO, Ojeda PB, Luna A, Pino MS, Avello BI, Carrera EL
Full text How to cite this article

Language: Spanish
References: 20
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PDF size: 105.53 Kb.


Key words:

newborn, prune-belly, obstructive uropathy.

ABSTRACT

The Prune-Belly syndrome is a distinct entity of unknown etiology, consisting of a spectrum of congenital malformations able to lead the pregnancy to abortion, or post-natal complications usually urinary of varying degrees of morbidity / mortality, which will determine the outcome of the infant born with this condition. Although it is a clinical picture with a very low mortality, the consequences are different for health and quality of infants life. In this research a case of Prune-Belly that was born at 36 weeks gestation, who presented the classic findings of this rare syndrome is reported.


REFERENCES

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