Quiros BC, Aragón GM

Language: Spanish
References: 10
Page: 723-728
PDF size: 198.30 Kb.

ABSTRACT

Thrombotic thrombocytopenic purpura (TTP). It is an acute and unpredictable onset pathology. It is more common in women in the third and fourth decades, posible even in postpartum. The diagnosis has always been difficult and the patient’s condition quickly worsens. Clinical laboratory could simplify the task of differencial diagnosis measuring ADAMTS 13 enzime activity in a pacient´s plasma. Once enzyme decrease activity has been proven, the presence of inhibitors can be measured, which could establish whether we are in the face of an autoinmune desorder. In the current work it is presented the first case in Costa Rica that manifest the presence of for ADAMTS 13 enzyme inhibitors as well as its subsequent clinical course.

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