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2003, Number 2

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Med Cutan Iber Lat Am 2003; 31 (2)

Birt-Hogg-Dube Syndrome

López-Escobar M, Gómez S, Manjón JA, Pérez N
Full text How to cite this article

Language: Spanish
References: 18
Page: 107-109
PDF size: 130.70 Kb.


Key words:

perifollicular fibromas, fibrofolliculomas, trichodiscomas, acrochordons, Birt-Hogg-Dube, Hornstein-Knickenberg.

ABSTRACT

Perifollicular fibromas, fibrofolliculomas and trichodiscomas are benign tumors of the hair follicle. We report the case of a 40-year-old man with spontaneous pneumothorax and multiple fibrofolliculomas (Birt-Hogg-Dube syndrome), and we discuss if these tumors could be histologic variations of a single lesion caused by interpretation of different sectioning planes.


REFERENCES

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Med Cutan Iber Lat Am. 2003;31