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ISSN 2007-3178 (Print)
Asociación Mexicana de Cirugía Bucal y Maxilofacial, Colegio Mexicano de Cirugía Bucal y Maxilofacial, A.C.

2015, Number 1

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Rev Mex Cir Bucal Maxilofac 2015; 11 (1)

Gorlin-Goltz syndrome: literature review and presentation of a series of clinical cases of a family of seven

Reyes ME, González FJM

Language: Spanish
References: 15
Page: 17-19
PDF size: 528.05 Kb.


ABSTRACT

The Gorlin-Goltz syndrome or naevoid basal cell carcinoma syndrome was first reported in 1894 by Jarisch and White, and later described by Gorlin and Goltz in 1960. It is characterized by a triad of multiple keratocysts, multiple nevoid basal cell epitheliomas and skeletal anomalies. We present a series of seven cases from the Zacatecas General Hospital, which focuses on the treatment of the keratocysts by the Maxillofacial Surgery Department, and in their early diagnosis based on major and minor clinical criteria, resulting in a variable- expressivity gene causing this disorder.


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