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2015, Number 2

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Rev Cubana Cardiol Cir Cardiovasc 2015; 21 (2)

Atrial myxomas in a patient with Carney syndrome

González GA, Naranjo UA, Selman-Housein SE, Frías GF, Seijas CA

Language: Spanish
References: 10
Page: 100-103
PDF size: 238.02 Kb.


ABSTRACT

Show a 14-year-old female patient treated at the William Soler Pediatric Cardiology Centre by fatigue. In complementary, she presented anemia and elevated ESR. Two-dimensional transthoracic echocardiography showed two tumors, one in the right atrium and the second in the left atrium. Removal is performed by right atrial transseptal approach using lung machine. Histopathological study showed that both tumors were myxomas. The patient had other tumors in skin, in external ear canal who were reported, as myxoma by biopsies performed. She was diagnosed as Carney syndrome.Five years later, recurrence myxoma in the right atrium that was removed. Eleven years after the first operation and six of the second, she is asymptomatic and free of tumors.


REFERENCES

  1. Carles JM, Ramírez JI, Hernández EB, Triana M, Santander M, Pomo M. Mixoma Auricular. Presentación de caso. Ga-ceta Médica Espirituana. 2008;10(3). Disponible en: http://bvs.sld.cu/revistas/gme/pub/vol.10.(3)_14/p14.html

  2. Abad C. Tumores cardíacos (I) Generalidades. Tumores pri-mitivos benignos. Rev Esp Cardiol. 1998; 51:10-20.

  3. Morillas P, Frutos A, Bertomeu V, Valero R, Rodríguez JA, Climent V, Moragón M. Un caso de síndrome de Carney. Rev Esp Cardiol. 2001; 54:803-6.

  4. Tápanes H, Senra L, Cotilla E, Ramiro JC, Naranjo AM, Pe-ña M. Mixoma ventricular derecho. Rev Fed Arg Cardiol. 2012; 41:205-7.

  5. Orozco DM, Abello M, Osorio JE. Severe mitral regurgita-tion following resection of a giant atrial myxoma: Case re-port and literature review. Rev Esp Anestesiol Reanim. 2013; 60:403-6. Disponible en: http://www.ncbi.nlm.nih.gov/pubmed/22748855

  6. Singh S, Singh M, Kovacs D, Benatar D, Khosla S, Singh H. A rare case of a intracardiac lipoma. Int J Surg Case Rep. 2015;9:105-8

  7. Vico L, Zúñiga E. Secondary pulmonary embolism to right atrial myxoma]. Semergen. 2013; 39:e54-56.

  8. Romanović R, Ratković N, Davičević Ž, Ilić R. Massive right atrial myxoma with dyspnea at rest in an elderly patient: a case report. Vojnosanit Pregl. 2015; 72:291-4. Disponible en: http://www.ncbi.nlm.nih.gov/pubmed/25958484

  9. Kirmani BH, Binukrishnan S, Gosney JR, Pullan DM. Left ventricular apical masses: distinguishing benign tumours from apical thrombi. Eur J Cardiothorac Surg. 2015 Mar 19. Disponible en: http://www.ncbi.nlm.nih.gov/pubmed/25792148

  10. Aval ZA, Ghaderi H, Tatari H, Foroughi M, Mirjafari SA, Forozeshfard M, et al. Surgical treatment of primary intra-cardiac myxoma: 20-year experience in "Shahid Modarres Hospital"--a tertiary university hospital--Tehran, Iran. Scien-tificWorldJournal. 2015; 2015:303629. Disponible en: http://www.ncbi.nlm.nih.gov/pmc/articles/PMC4321676/




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