Negrín VT, Lage LLM, Quintana CGR, Santos PA, Valero HA

Language: Spanish
References: 15
Page: 229-234
PDF size: 375.87 Kb.

ABSTRACT

Arrhythmogenic right ventricular dysplasia is a heart muscle disease that predominantly affects the right ventricle, bringing about the replacement of normal myocardium with fatty or fibrofatty tissue and causing sudden death in young individuals. Ventricular tachycardia is an important clinical manifestation, although there are reports of right or global heart failure. The diagnosis is confirmed by echocardiography and magnetic resonance imaging. The case of a 65-year-old former smoker, with hypertension and ischemic heart disease, a history of effort syncope symptoms and proven non-sustained ventricular tachycardia, with morphology of left bundle branch block, is reported. Relevant diagnostic studies were performed, and echocardiographic elements which were compatible with arrhythmogenic right ventricular dysplasia were found. Therefore, an implantable cardioverter defibrillator was implanted, after which the patient has had a favorable outcome.

REFERENCES

1. Marcus FI, McKenna WJ, Sherrill D, Basso C, Bauce B, Bluemke DA, et al. Diagnosis of arrhythmogenic right ventricular cardiomyopathy/dysplasia: proposed modification of the Task Force Criteria. Eur Heart J. 2010;31:806-14.

2. Morales LM, Jerez AM, San Román E. ¿Displasia Arritmogénica del ventrículo derecho o enferme-dad de Uhl? Rev Fed Arg Cardiol. 2012;41:59-60.

3. Capulzini L, Brugada P, Brugada J, Brugada R. Arrit-mias y enfermedades del corazón derecho: de las bases genéticas a la clínica. Rev Esp Cardiol. 2010; 63:963-83.

4. Basso C, Corrado D, Marcus FI, Nava A, Thiene G. Arrhythmogenic right ventricular cardiomyopathy. Lancet. 2009;373:1289-300.

5. Pérez A, Zuelgaray G. Muerte súbita en deportistas: Importancia del reconocimiento de las miocardio-patías. Insuf Card. 2009;4(3):130-5.

6. Fontaine G, Frank R, Guiraudon G, Pavie A, Tereau Y, Grosgogeat Y. The significance of intraventricular conduction defects in arrhythmogenic right ventri-cular dysplasia. En: Levy S, Scheinman M, eds. Car-diac Arrhythmias: From Diagnosis to Therapy. Mount Kisco, NY: Futura; 1984. p. 233-9.

7. Pérez AR, Schapachnik E, Dubner S, Baranchuk A. El valor del electrocardiograma en el diagnóstico de las enfermedades eléctricas primarias o canalopa-tías sin cardiopatía estructural aparente. Primera parte: el síndrome de Brugada. Rev Fed Arg Cardiol. 2010;39:8-15.

8. Hershberger RE, Cowan J, Morales A, Siegfried JD. Progress with genetic cardiomyopathies: Screening, counseling, and testing in dilated, hypertrophic, and arrhythmogenic rightventricular dysplasia/car-diomyopathy. Circ Heart Fail. 2009;2:253-61.

9. Brugada R. La muerte súbita en el corazón sano. Rev Esp Cardiol. 2010;10:A78-84.

10. 10.Albina G, Laíño R, Giniger A. Displasia arritmogénica del ventrículo derecho: revisión de una enferme-dad poco común con un espectro variado de pre-sentaciones clínicas. Electrofisiol Arritm. 2009;4: 139-44.

11. 11.Markel TA, Wairiuko GM, Lahm T, Crisostomo PR, Wang M, Herring CM, et al. The right heart and its distinct mechanisms of development, function, and failure. J Surg Res. 2008;146:304-13.

12. 12.Sen-Chowdhry S, Prasad SK, Syrris P, Wage R, Ward D, Merrifield R, et al. Cardiovascular magnetic reso-nance in arrhythmogenic right ventricular cardio-myopathy revisited: comparison with task force criteria and genotype. J Am Coll Cardiol. 2006;48: 2132-40.

13. 13.Moya A, Sancho-Tello MJ, Arenal Á, Fidalgo ML, Brugada R, Martínez Ferrer J, et al. Novedades en alteraciones del ritmo cardiaco: electrofisiología cardiaca, arritmias y estimulación cardiaca. Rev Esp Cardiol. 2013;66:116-23.

14. 14.Alzueta J, Fernández JM. Registro Español de Desfi-brilador Automático Implantable. VIII Informe Oficial del Grupo de Trabajo de Desfibrilador Automá-tico Implantable de la Sociedad Española de Cardio-logía (2011). Rev Esp Cardiol. 2012;65:1019-29.

15. 15.Castellá M, Nadal M. Indicaciones de la cirugía en el tratamiento de las taquiarritmias. Guías clínicas. Cir Cardiov. 2010;17:143-52.