Left diaphragmatic hernia: about a case

Silvia Evelyn Jiménez Abreu; Aniubis Fleitas Cabrera; Osmani Martínez Lemus; Jorge Alexis Pérez González; Sualy Ruiz Morera

2014, Number 2

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Cuba y Salud 2014; 9 (2)

Left diaphragmatic hernia: about a case

Jiménez ASE, Fleitas CA, Martínez LO, Pérez GJA, Ruiz MS

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Language: Spanish
References: 17
Page: 42-45
PDF size: 383.00 Kb.

ABSTRACT

Congenital diaphragmatic hernia is one of the most severe malformations of the newborn, resulting from abnormal development of the fetal diaphragm that allows the abdominal viscera to invade the thoracic cavity and interfere in the correct pulmonary growth causing hypoplasia of this organ and persistent pulmonary hypertension, very commonly untreatable. It occurs in 1 per 2500 of livebirth infants, and can be frequently diagnosed by ultrasoundgraphy in early gestation stages. The hereditary pattern is multifunctional. Malformation is associated to chromosomal abnormities and high mortality. Clinical manifestations range from a severe respiratory failure at birth to a finding, depending on hypoplasia and pulmonary hypertension grade. A case of a newborn with a left congenital diaphragmatic hernia post-natal diagnosis, which starts with respiratory difficulty and cyanosis in the first minutes of being born birth, is presented. Surgical treatment with a complete recovery was successful. Due to this malformation severity and its possible consequences, it is considered important letting the case to be known, with the purpose of contributing to a better improvement of the pre-natal diagnosis programs.

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