Luna-Vicencio A, Guerrero-Avendaño G

Language: Spanish
References: 10
Page: 389-394
PDF size: 442.00 Kb.

ABSTRACT

Suprarenal myelolipoma is a benign tumor extremely rare in children, which is associated with endocrine dysfunction and may simulate other neoplasms such as Wilms’ tumor; in the English-language literature only 3 cases have been reported in children under 16 years.
Material and method: Adolescent female patient age 16 years with plethoric facies (full-moon face), hirsutism, and body hair with android distribution. Image studies showed a suprarenal tumor. Two surgeries were performed (incisional biopsy of right kidney and, subsequently, radical nephrectomy). The second histopathological report concluded suprarenal tumor with histological characteristics of myelolipoma.
Discussion: Everything we know about myelolipoma has been described in adults. If the tumor is of suprarenal origin and of considerable size it may simulate a Wilms’ tumor in pediatric patients. However, image studies help to properly evaluate its characteristics and growth pattern.
Conclusion: Suprarenal myelolipoma, a rare pathology in children, should be considered as a differential diagnosis in evaluating retroperitoneal tumors.

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