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2002, Number 3

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Rev Inst Nal Enf Resp Mex 2002; 15 (3)

Lymphangioleiomyomatosis. Case presentation and literature review.

Laniado-Laborín R, Valenzuela-Espinoza A, Cabrales-Vargas MN

Language: Spanish
References: 10
Page: 162-165
PDF size: 92.15 Kb.


ABSTRACT

Lymphangioleiomyomatosis (LAM) is a rare disease that exclusively affects women. It is characterized by the abnormal proliferation of atypical smooth muscle cells, which gradually occlude airways, and lymphatic and blood vessels. A case of a 32-year Mexican female, with a history of recurrent bilateral pneumothorax is presented. The thorax CT scan revealed numerous thin-walled cystic lesions throughout both lung fields. Lung biopsy specimens evaluated by immunohistochemical staining contained LAM cells that were positive for HMB-45.


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