Sánchez LV, García GAD, Nazco FG, Gómez DY, Márquez PN

Language: Spanish
References: 9
Page:
PDF size: 67.43 Kb.

ABSTRACT

Background: The non-bullous congenital ichthyosiform erythroderma is a genodermatosis that is present from the birth and the vegetating pemphigus is a bullous disease that occurs at early ages of life, the clinical manifestations of these entities are different, both are uncommon when they are presented in isolation, much more when they appear in a patient. Objective: To describe the case of a patient with a non-bullous congenital ichthyosiform erythroderma and vegetating pemphigus a strange clinical situation for their incidence. Case presentation: Patient of 28 years, with antecedents of suffering of non-bullous congenital ichthyosiform erythroderma that began to develop blisters and when breaking they left erosions that later gave place to hypertrophic and papillomatous vegetation. To arrive to the diagnosis was kept in mind the clinical approach and the histopathology. Conclusions: The non-bullous congenital ichthyosiform erythroderma and the vegetating pemphigus are uncommon entities in the medical practice, much more when both are presented in a patient.

REFERENCES

1. Manzur Katrib J, Díaz Almeida JG, Cortés Hernández M, Ortiz González PR, Sagaró Delgado B,Abreu Daniel A, et al. Dermatología. 1ra.ed. La Habana: Editorial Ciencias Médicas;2002.

2. Odom R, James N, Berger T. Dermatología Clínica de Andrews, 9na. ed. Madrid: Marban Libros SL;2004.

3. Fitzpatrick TB. Hiperqueratosis epidermolítica. En: Dermatología en Medicina General. 6ta.ed. Buenos Aires: Médica Panamericana; 2007.

4. Arenas R. Dermatología, atlas, diagnóstico y tratamiento. 3ra. Ed. México: McGraw-Hill; 2004. p. 447-51.

5. Larangeira H, Pereira MG, Maffei I, Aoki V. Pemphigus vegetans associated with verrucous lesions-expanding a phenotype. Clinics (Sao Paulo) [Internet]. 2006 Jun [cited: 2014 Mar 2];61(3):279-82. Available from: http://www.scielo.br/scielo.php?script=sci_arttext&pid=S1807- 59322006000300016&lng=en&nrm=iso&tlng=en

6. Herrera I, Miranda J. Pénfigo vulgar. Criterios actuales. Rev haban cienc méd [Internet]. 2009 Dic [citado 2 Mar/ 2014]; 8(5 supl.5). Disponible en : http://scielo.sld.cu/scielo.php?script=sci_arttext&pid=S1729- 519X2009000500008&lng=es&nrm=iso&tlng=es

7. Chams-Davatchi C, Esmaili N, Daneshpazhooh M, Valikhani M, Balighi K, Hallaji Z, et al. Randomized controlled open-label trial of four treatment regimens for pemphigus vulgaris. J Am Acad Dermatol [Internet]. 2007 Oct [cited 2014 Mar 2];57(4):622-8. Available from: http://www.jaad.org/article/S0190-9622%2807%2900890-0/pdf

8. Hatano Y, Ishikawa K, Koga H, Ishii N, Hashimoto T, Takeo N, et al. A case of concurrent pemphigoid vegetans and pemphigus vegetans remitted without oral corticosteroid. Br J Dermatol [Internet]. 2014 May [cited 2014 Mar 2];170(5):1192-4. Available from: http://www.ncbi.nlm.nih.gov/pubmed/24359309

9. Dahbi N, Hocar O, Akhdari N, Amal S, Fakhri A, Rais H, Belaabidia. Pemphigus vegetans: Rare form of pemphigus. Presse Med. 2014 May;43(5):619-21. Disponible en : http://www.ncbi.nlm.nih.gov/pubmed/24613065