Bósquez D, Martíz AA, McKeever C, Ríos YJM

Language: Spanish
References: 16
Page: 71-74
PDF size: 461.14 Kb.

ABSTRACT

Dermatofibrosarcoma protuberans (DFSP) is an uncommon malignant mesenchymal tumor that arises in the dermis and is characterized by a prolonged latency which delays its detection. The atrophic or morphea-like DFSP is a rare form of the disease that resembles other benign lesions such as morphea, idiopathic atrophoderma, atrophic scar, anetoderma or lipoatrophy. It behaves like classic DFSP and commonly affects young to middle aged adults. It has a slow infiltrative growth pattern and a high rate of local recurrences if not completely excised. Metastases are rare and occur after multiple local recurrences. Surgical excision is the first line of treatment. Long term follow up is required to detect recurrence. We report a case of an atrophic DFSP in which the diagnosis was achieved according to clinical, histopathological and immunohistochemical findings. The tumor was completely excised with safety margins and the patient is currently under follow up.

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