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ISSN 1561-3194 (Electronic)

2016, Number 2

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Rev Ciencias Médicas 2016; 20 (2)

Neurofibromatosis type-I involving the upper maxilla

Carmona FE

Language: Spanish
References: 11
Page: 249-254
PDF size: 267.83 Kb.


ABSTRACT

Introduction: Von Recklinghausen disease or neurofibromatosis type I is an autosomal dominant disease with a wide clinical expression, with manifestations ranging from multiple café-au-lait spots to severe functional and aesthetic complications affecting bone tissue and nerve. Oral manifestations of neurofibromatosis type I are rare, affecting some patients.
Case report: a case presenting neurofibromatous lesions in the upper alveolar ridge, maxillary tuberosity and part of the pterygomaxillary cavity, indicating surgical excision due to the difficulties presented when using dental prosthesis and the risk of trauma for this tumor during the mastication process. The relevance of this research lies in the fact that the disease rarely occurs in oral cavity. The size of the tumor, the surgical approach applied and the functional and aesthetic results obtained are shown, with no evidence of recurrence to date.
Conclusions: a case of neurofibromatosis was presented, located in the alveolar ridge, maxillary tuberosity and pterygomaxillary cavity. Treatment made possible the functional and aesthetic rehabilitation of the patient.


REFERENCES

  1. Rodrigues G, Joaquim A, Ghizoni E, Queiróz L, Tedeschi H. Giant Cervical NeurofibromawithConcomitantDeformity - SurgicalStrategiesfortreatment. J. bras. Neurocir [Internet]. 2013 [Citado 2014 Oct 15]; 23(4): [Aprox. 8 p.]. Disponible en: http://www.abnc.org.br/ed_art_down.php?id=1031

  2. Sethi A, Chopra S, Passey JC, Agarwal AK. Intraparotid Facial Nerve Neurofibroma: an Uncommon Neoplasm. Int. J. Morphol. [Internet]. 2011 Sep [citado 2014 Oct 15]; 29(3): [Aprox. 6 p.]. Disponible en: http://www.scielo.cl/scielo.php?script=sci_arttext&pid=S0717-95022011000300066

  3. Vargas Domínguez R, Díaz Zavala FA, Beltrán Ortega C. Neurofibroma en paladar Reporte de un caso. OdontAct [Internet]. 2012 [citado 2014 Jul 08]; 9(115): [Aprox. 4 p.]. Disponible en: http://www.imbiomed.com.mx/1/1/articulos.php?method=showDetail&id_revista=306&id_seccion=4703&id_ejemplar=8739&id_articulo=88848

  4. Orraca Castillo M, Licourt Otero D. Características del neurofibroma plexiforme en pacientes con neurofibromatosis tipo 1. Pinar del Río. Revista de Ciencias Médicas de Pinar del Río [Internet]. 2012 [citado 2014 Jul 8]; 16(4): [Aprox. 10 p.]. Disponible en: http://www.revcmpinar.sld.cu/index.php/publicaciones/article/view/953 /html

  5. Duque FL, Ramírez OA. Neurofibromatosis: a case report. RevFacOdontolUnivAntioq [Internet]. 2010 [citado 2014 Jul 08]; 21(2): [Aprox. 16 p.]. Disponible en: http://aprendeenlinea.udea.edu.co/revistas/index.php/odont/article/view/2556 /4863

  6. Bermeo Herrera R, Molina Solano B, Bermejo González N. Neurofibromatosis Tipo 1 o Enfermedad de Von Recklinghausen: Reporte de un caso y revisión bibliográfica. Oncología [Internet]. 2010 [citado 2014 Jul 08]; 20(3-4): [Aprox. 6 p.]. Disponible en: http://www.imbiomed.com.mx/1/1/articulos.php?method=showDetail&id_revista=107&id_seccion=1606&id_ejemplar=7420&id_articulo=74390

  7. Duque FL, Ramírez OA. Neurofibromatosis: a case report. RevFacOdontolUnivAntioq[Internet]. 2010 [citado 2014 Jul 08]; 21(2): [Aprox. 16 p.]. Disponible en: http://aprendeenlinea.udea.edu.co/revistas/index.php/odont/article/view/2556 /4863

  8. 8.Vaillant Suárez GM, Pereira Gómez G. Neurofibromatosis de von Recklinghausen en la niñez. MEDISAN [Internet]. 2010 Jul [citado 2014 Jul 08]; 14(5): Disponible en: http://scielo.sld.cu/scielo.php?script=sci_arttext&pid=S1029 -30192010000500017&lng=es

  9. 9.Orraca Castillo M, Travieso Téllez A . Caracterización clínica de pacientes con neurofibromatosis segmentaria. Revista de Ciencias Médicas de Pinar del Río [Internet]. 2012 Jul [citado 2014 Jul 07]; 16(2): [Aprox. 5 p.]. Disponible en: http://scielo.sld.cu/pdf/rpr/v16n2/rpr06212.pdf

  10. Salas Alanis JC, De la Garza Ramos R, Cepeda Valdés R. Neurofibromatosis Tipo 1 (enfermedad de von Recklinghausen): reporte de 2 casos Dermatología CMQ [Internet]. 2011 [citado 2014 Jul 08]; 9(4): [Aprox. 6 p.]. Disponible en: http://www.imbiomed.com.mx/1/1/articulos.php?method=showDetail&id_revista=209&id_seccion=3502&id_ejemplar=7595&id_articulo=76377

  11. Javed F, Ramalingam S, Bashir Ahmed H, Gupta B, SundarCh, Qadri T, et al. Oral manifestations in patients with neurofibromatosis type-1: A comprehensive literature review. Critical Reviews in Oncology Hematology.[Internet]. 2014 [citado 2014 Jul 08]; 91(2): [Aprox. 6 p.]. Disponible en: http://fawadjaved.com/wp-content/themes/fawad/downloads /Javed%20et%20al%202014%20(NF%20&%20Oral%20health).pdf




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