Salazar TL, Díaz MC, Quintana GF, Batista HNE

Language: Spanish
References: 10
Page: 306-309
PDF size: 93.82 Kb.

ABSTRACT

Hereditary angioedema is a primary immunodeficiency disease due to a deficiency in the complement system, which is characterized by recurrent episodes of swelling that may affect the skin, mucosas and submucosal tissues. Abdominal pain associated with angioedema can be confused with an acute abdomen and leads to an unnecessary surgery. Laryngeal edema means a risk for the patient's life, because it can cause death due to suffocation. Hormonal variations in women seem to have a high incidence on this disease. This edema does not respond to treatment with steroids and antihistamines, that’s why it has to be differentiated from allergic edema in order to know how to treat it. The appropriate diagnosis of this disease is necessary to establish the adequate treatment and to reduce the risk of death; therefore education of the medical staff in relation to this affection is very important because of the high incidence in this province.

REFERENCES

1. Bousfiha AA, Jeddane L, Ailal F, Al Herz W, Conley ME, Cunningham-Rundles C, et al. A phenotypic approach for IUIS PID classification and diagnosis: guidelines for clinicians at the bedside. J Clin Immunol. 2013;33(6):1078-87.

2. Velasco-Medina AA, Cortés-Morales G, Barreto-Sosa A, Velázquez-Sámano G. Fisiopatología y avances en el tratamiento del angioedema hereditario. Rev Alergia Méx [internet]. 2011 [citado 12 ene. 2015];58(2):[aprox. 8 p.]. Disponible en: http://cmica.org.mx/wpcontent/ uploads/2016/01/REVISTA-2-2011.pdf#page=40

3. Cicardi M, Bork K, Caballero T. On behalf of HAWK* (Hereditary Angioedema International Working Group). Evidence-based recommendations for the therapeutic management of angioedema due to hereditary C1- inhibitor deficiency. Consensus report of an International Working Group. Allergy. 2012; 67:147-57.

4. Superintendencia de Servicios de Salud. Res. 1200/2012. Créase Sistema Único de Reintegros. Normas Generales. Limítase vigencia temporal de normas -APE-. Bol Oficial N: 32.493. Argentina: Ministerio de Salud; 2012 oct. 3.

5. Caballero T, Farkas H, Bouillet L, Bowen T, Gompel A, Fagerberget C. et al . International consensus and practical guidelines on the gynecologic and obstetric management of female patients with hereditary angioedema caused by C1 inhibitor deficiency. J Allergy Clin Immunol [internet]. 2012 Feb.; 129(2):[aprox. 13 p.]. Disponible en: http://www.sciencedirect.com/science/article/pii/S0091674911018306

6. Al Awad A, Galban JT, Ocando M, Loero A, Molero F. Angioedema hereditario: causa rara de dolor abdominal. Cir Esp. 2012;90:261-72.

7. Salas-Lozano NG, Meza-Cardona J, González-Fernández C, Pineda-Figueroa L, de Ariño- Suárez M. Angioedema hereditario: causa rara de dolor abdominal. Cir Cir [internet]. 2014 sep.- oct. [citado 6 dic. 2015];82(5):[aprox. 4 p.]. Disponible en: http://eds.a.ebscohost.com/eds/pdfviewer/pdfviewer?sid=8d2305f6-dad9-4bc7-883b- 4fabbef6458e%40sessionmgr4009&vid=1&hid=4110

8. Malbrán A, Fernández Romero DS, Menéndez A. Angioedema hereditario. Guía de tratamiento. Medicina (Buenos Aires) [internet]. 2012 [citado 6 dic. 2015];72(2):[aprox.5 p.]. Disponible en: http://medicinabuenosaires.com/revistas/vol72-12/2/vol.%2072_n2_p.%20119-123-med2-10- .pdf

9. Zuraw BL, Banerji A, Bemstein JA. US Hereditary Angioedema Association Medical Advisory Board 2013 .Recommendations for the Management of Hereditary Angioedema Due to C1 Inhibitor Deficiency. J Allergy Clin Imunol Practice. 2013;1:458-67.

10. Malbrán A, Malbrán E, Menéndez A, Fernández Romero DS. Angioedema hereditario. Tratamiento del ataque agudo en la Argentina. MEDICINA (Buenos Aires) [internet]. 2014 [citado 21 nov. 2015];74:[aprox. 4 p.]. Disponible en: http://www.aehargentina.org/descargas/AEH-Tratamiento-Ataque-Agudo-Argentina.pdf