2017, Number 2
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Rev Med Inst Mex Seguro Soc 2017; 55 (2)
Type I Chiari malformation associated with cerebellar atrophy. Case Report
Moscote-Salazar LR, Calderón-Miranda WG, Alvis-Miranda HR, Lee-Aguirre Á, Alcalá-Cerra G
Language: Spanish
References: 11
Page: 260-263
PDF size: 261.25 Kb.
ABSTRACT
Chiari malformation is characterized by caudal displacement
of the cerebellar tonsils that penetrate into
the spinal canal through the foramen magnum, achieving
reach the atlas or axis. trunk and any drop of the
fourth ventricle is observed. Typically is seen in young
adults. In some cases scoliosis and Syringomyelic
cavities may occur.
The authors present (as far as they know) the first case
in the literature with long term follow-up, of a caucasian
woman with an unusual form of cerebellar atrophy and
Chiari Type I malformation, suffering from weakness in
his upper and lower extremities with rapidly progression.
The patient was successfully treated with suboccipital
decompression and C1 laminectomy.
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