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ISSN 2683-1678 (Print)
Órgano Oficial de la Sociedad
Latinoamericana de lnfectología Pediátrica.
Órgano de la Asociación Mexicana de
Infectología Pediátrica, A.C.
Órgano difusor de la Sociedad Española
de lnfectología

2017, Number 1

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Rev Latin Infect Pediatr 2017; 30 (1)

Secondary fulminant hepatitis a hemochromatosis neonatal, differential diagnosis: case report and review of literature

Kuri AS, Montaño RD, Zárate MF, Montijo BE, Cervantes BR, Ramírez MJA

Language: Spanish
References: 22
Page: 32-36
PDF size: 188.88 Kb.


ABSTRACT

Fulminant hepatitis is acute failure characterized by prolonged clotting times (prothrombin time › 17 seconds or ‹ 50%) with or without liver function encephalopathy. Being the most common cause of infectious etiology, followed by autoimmune process and ending with metabolic diseases. Neonatal hemochromatosis is one of the rare causes of liver failure in the newborn because of not well known. Characterized by deposition of iron in the liver and extrahepatic tissues, with some deposition in the reticuloendothelial system in the absence of hemolytic disease syndromes associated with massive deposition of iron or iron overload exogenous. It is a serious disease responsible for high fetal and neonatal mortality, and today it is being recognized as a major cause of cirrhosis and liver failure perinatal. We report the clinical case of a female of 44 days of age with liver failure and histopathological report of neonatal hemochromatosis in order to alert the clinician to optimize early diagnosis and management.


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