Sarmiento-Martínez HI, Martínez-García E, Vázquez-Cervantes ME, Comparan-Martínez JL, Chávez-Ruiz R, Ramírez-de la Peña JL, Aguilar-Morales EF, Muñiz-Ugarte JG, Muñoz-González R

Language: Spanish
References: 12
Page: 251-259
PDF size: 552.23 Kb.

ABSTRACT

Portal hypertension is defined as pressure in the portal vein over 5 mmHg. It is classified as prehepatic, hepatic, and post-hepatic. The predominant type in children is prehepatic, with an incidence of 61.5%, reporting cavernous transformation of the portal vein as its primary cause in Mexico. Cavernous transformation of the portal vein is a condition characterized by the formation of a network of dilated collateral veins along a previously thrombosed portal vein. We present two pediatric clinical cases: a girl age 3 years who presented onset of abdominal pain and vomiting and a boy age 13 years who presented onset of thrombocytopenia and abdominal pain; both were diagnosed by abdominal ultrasound and their diagnoses were corroborated by CT angiography. It is important that the radiologist and treating physicians be familiar with this disease so that the patient can be referred to a specialized care facility for timely diagnosis and treatment.

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