Gómez Llata GS, Padrón SN, González HFJ

Language: Spanish
References: 6
Page: 131-134
PDF size: 99.88 Kb.

ABSTRACT

The Langerhans cell histyocitosis, X histyocitosis, Langerhans cell granuloma, or eosinophilic granuloma,1 is a pseudotumoral pathology of a diseases group denominated reticuloendoteliosis.2 The incidence is 0.05 to 0.5% in children for year in United States, male predominate 2:1, can presented as solitary or multiple lesion. The major frequency is in the infancy between 5 and 10 year age, the major frequency of localization is skull, ribs, spine, pelvis or tubular bone. Histological characteristics a whole of histyocitic cell equal to the skin this derivate in grant cell with five or 7 nucleus. The malignant behavior is bigger among more young is the patient. The objective is a case report of histyocitosis Langerhans cell in pediatrics patient of 17 months age, the initial syntoms is irritation and tumefaction without fever with 24 hours of evolution. The X-ray showed solitary lesion in shaft the femur right. We realized incision biopsy for the hystopatological diagnosis. The treatment consisted in curettage and homologous graft of mother iliac crest, immobilization with callouts cast for six weeks, with radiographic control, this showed graft integration and not developed of lesion.

REFERENCES

1. Greenspan A, Remagen W. Tumores de huesos y articulaciones. Edit Marban; 2002, p. 247.

2. Coppes R, Zantinga E. The Langerhans cell histiocitosis X files revealed. Br J Haematol 2002; 116: 3-9.

3. Greenspan A, Remagen W. Tumores de huesos y articulaciones. Edit Marban; 2002, p. 247.

4. Donadieu J. A multicentre retrospective survey of Langerhans’ cell histiocytosis: 348 cases observed between 1983 and 1993.

5. Broadvent V. Favourable prognosis features in histiocytosis X: bone involvement and absence of skin disease. Arch Dis Child 1986; 61: 1219-21.

6. Lichtenstein L, Jaffe H. Eosinophilic granuloma of bone, marrican. J Phatol; 16: 595-607.