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Órgano Oficial del Instituto Nacional de Pediatría

2017, Number 6

Acta Pediatr Mex 2017; 38 (6)

Pediatric hepatopulmonary syndrome. Case report and a literature review

López-Birlain L, Cuevas-Schacht FJ, Gutiérrez-Morales G, Alva- Chaire AC

Language: Spanish
References: 11
Page: 371-377
PDF size: 1090.46 Kb.


ABSTRACT

The hepatopulmonary syndrome is an infrequent disease in pediatric population, with an unknown incidence in Mexico. The diagnosis is a challenge for the clinician due to the presence of many other causes of hypoxemia in children with chronic liver disease.
Two patients with Hepatopulmonary Syndrome are presented, showing the variability in both cases and outcome of the disease. First a patient with chronic liver disease secondary to an autoimmune disease (Systemic Lupus Erythematosus) with a torpid evolution, then a patient in which the diagnosis of chronic liver disease was made after the onset of the respiratory symptoms. In both cases the ideal treatment should be hepatic transplantation, however it could not be done because of the low accessibility to this surgical procedure in our country.


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