Manzo-Ríos MA, Anaya-García JE

Language: Spanish
References: 9
Page: 133-137
PDF size: 79.71 Kb.

ABSTRACT

Introduction: There are many types of Congenital Heart Disease, some of them simple or complex. Cor Triatriatum (CT) is a congenital anomaly very unusual.There is a pulmonary vein common chamber (proximal chamber) separated from the left atrium (distal chamber) by a fibromuscular septum. There is a communication in the majority of the cases by one o more holes between the two chambers. The clinical aspects in CT depends on the orifices size. In most cases the orifices are very restrictive and more than 75% die in the first year of life.
Clinical Case: A 3 month old male who started 20 days before, with a history of respiratory distress, with the conclusion of pneumonic disease. He was discharged from the regional center and came back later. Now he has a heart murmur and bad conditions, they decide to send him to our Hospital. He required endotraqueal intubation for his condition, a systolic murmur in the fourth intercostal space Grade I/VI was heard, and hiperdinamic bulge was noted. After the studies was made we conclude diagnostic of CT. We summited him to surgery repair and his condition was very good and was discharged.
Conclusions: Cor Triatriatum is an unusual pathology that can be confused easily with pulmonary infection disease and with other heart diseases that produce obstruction of the arrival of pulmonary veins. The Echocardiogram is the clue to make diagnosis and define the different anatomical types. The earlier we make the diagnosis and surgery, better is the outcome.

REFERENCES

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