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2019, Number 1

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Ann Hepatol 2019; 18 (1)

Type II Abernethy Malformation in a Patient with Primary Budd-Chiari Syndrome

Ding Peng-Xu, Han Xin-Wei, Liu C

Language: English
References: 12
Page: 246-249
PDF size: 419.30 Kb.


ABSTRACT

Budd-Chiari syndrome (BCS) is a heterogeneous group of disorders characterized by hepatic venous outflow obstruction. Abernethy malformation is a congenital vascular malformation defined by diversion of portal blood away from the liver. Both conditions are rare vascular diseases. We report here the first case of a patient with combined type II Abernethy malformation and BCS from China. The inferior vena cava obstruction was treated with percutaneous balloon angioplasty; close follow-up was elected for the Abernethy malformation.


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