Rodríguez-Cabrera L, Zuazo F, Schneider-Ehrenberg O, Moreno-García A, Tovilla-Canales JL

Language: Spanish
References: 10
Page: 39-43
PDF size: 434.68 Kb.

ABSTRACT

Myxomas are rare, benign tumors of mesenchymal origin, which can be found in skin, heart, subcutaneous tissue and bone. Here we describe the case of an orbital myxoma and present it’s clinical and imaging characteristics, as well as the surgical approach and histopathological description that led us to the diagnosis. Fourty year old male with a history of progressive swelling in the inner third of the left lower eyelid for 5 months. Previously, the patient had undergone resection of a tumor in the same region with histopathological diagnosis of rhabdomyosarcoma. At examination a soft, mobile, painless mass was found in the inner third of the left lower eyelid, which did not change with Valsalva maneuver. Computed tomography showed a homogeneous extraconal lesion, similar to the density of the vitreous, with well-defined edges, in the anterior and inferonasal portion of the left orbit. Excisional biopsy was performed, and subsequent histopathology showed fusiform cells without nuclear atypia and abundant myxoid stroma. Its immunohistochemistry was positive for vimentin and S-100. With this, an orbital myxoma was diagnosed. After surgery, the patient progressed well and was asymptomatic and without recurrence of the tumor.

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