Argüello RV, Rico NA, Gutiérrez RF, Martínez RDA, Pliego MR, Espinosa SJA

Language: Spanish
References: 6
Page: 43-47
PDF size: 194.98 Kb.

ABSTRACT

The Askin’s tumor is a rare neoplasm of the chest wall that belongs to the group of primitive neuroectodermal tumors (PNETs), which are derivatives from neuroectodermal pluripotent neural crest cells. The range of this type of tumors covers from Ewing’s sarcoma to the neuroepithelioma and they belong to the group of small round blue cells tumors which are characterized for having an aggressive behavior with diverse clinical manifestations depending on their anatomical location.
The most common locations for the Askin’s tumor is the thoracopulmonary area followed by the pelvic area and in the case of metastases the lungs, bones, liver and brain are the most affected parts.
In order to identify this disease, the diagnosis of this type of tumor consists on image studies and the confirmation is made through a hispathology biopsy or surgical resection.

REFERENCES

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