Miranda-Aquino T, Castro-Gallegos PE, Pineda-De Paz DO, Machuca-Hernández M, James-Santana JR, Lomelí-Sánchez OS, Hernández-del Río JE, González-Padilla C

Language: English
References: 10
Page: 34-37
PDF size: 274.80 Kb.

ABSTRACT

A 17-year-old female was admitted to the hospital with progressive shortness of breath. It started three weeks before admission, and initially presented only on moderate exertion, worsening until it was present at rest and accompanied with orthopnea. Five days before admission, she developed hemoptysis. Three days before, she had a syncope and was taken to the emergency department of a nearby hospital. After she was examined, an acute abdominal pain secondary to cholecystitis was diagnosed. Cholecystectomy was performed and as an additional finding, surgeons reported hepatomegaly and took a liver biopsy. After these, an abdominal and chest computed tomography (CT scan) with IV contrast was performed, where a right atrial tumor with pericardial extension was reported. Based on this, they decided to perform a transthoracic echocardiogram and discovered a hyper-echogenic right atrial tumor, covering the entire cavity and protruding through the tricuspid valve. She was transferred to our hospital and taken to cardiac surgery due to worsening heart failure symptoms, where 80% of the tumor was resected. A high grade leiomyosarcoma was reported. A couple weeks later, the patient died secondary to refractory septic shock.

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