2019, Number 4
Rev Fac Med UNAM 2019; 62 (4)
Langerhans’ cell histiocytosis in their orbitfocused presentation. Review of the topic regarding a case
Dávila MR, Figueroa FA, Ontiveros VF, Urbina SA
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ABSTRACTObjective: To describe a case of Langerhans cell histiocytosis in a pediatric patient.
Method: A 4-year-old patient with proptosis, diplopia, fever and loss of visual acuity, with evident image in a computed tomography of orbital mass with bone erosion. An excisional biopsy was performed by coronal craniotomy. The histopathological result was Langerhans cell histiocytosis.
Results: The anatomopathological study showed a neoplasm of small round and blue cells, compatible with Rhabdomyosarcoma. Immunohistochemical tests concluded the diagnosis of Langerhans cell histiocytosis.
Conclusion: Langerhans cell histiocytosis is a rare disease that requires clinical suspicion and a timely diagnosis to adjust the treatment and improve the survival of patients.