Segura-Hernández M, Pérez-Chirino EG, Sánchez-Valerio AP, Lino-González AL

Language: Spanish
References: 16
Page: 128-133
PDF size: 286.52 Kb.

ABSTRACT

Bulboespinal muscular atrophy or Kennedy disease is a rare condition of the motor neuron. Patients with this condition, in addition to presenting motor problems that substantially affect their autonomy, will present to a greater or lesser extent affectations related to the musculature of the phonoarticulator mechanism, causing problems in the production of speech, voice and the function of swallowing. Evaluation and intervention by the phoniatric specialist is essential to establish intervention strategies aimed at communication skills and safe food ingestion.

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