Cruz SR, Bencomo GD, Valladares BA, Arredondo CC

Language: Spanish
References: 11
Page: 133-141
PDF size: 387.93 Kb.

ABSTRACT

Meliomeningocele is a major congenital malformation frequently associated with an important morbimortality, this is an affection caused by a flaw in the closure of the neural tube in the first weeks of pregnancy. The natural history of the disease is death due to infection of the central nervous system and/or a degree of an advanced motor or sensitive incapacity. The case to be presented is a female newborn, cephalic presentation, Apgar 9,10, 10. Weight 3250g, size 51 cm, cranial circumference 34 cm, thoracic circumference 35 cm, meconio ++, On the physical examination as positive data mounted sutures, tumorations the size of an orange at the lumbosacral level were found and also feet calcareous baro, and normal motility in lower limbs. The tumorations was covered with sterile dressing and the patient was transferred to a hospital of the capital city with a diagnosis of lumbosacral Mielomeningocele and calcareous feet for further studies. In this case a surgical intervention with a ventricular peritoneal derivation of the hydrocephaly should be done, correction of the Mielomeningocele and correction of the equine bilateral baro feet. The early diagnosis of congenital malformations by means of prenatal ultrasound scans can reduce the incidence of these affections by means of the interruption of pregnancy in the first trimester, and this constitutes one of the main achievements of the Mother-infant Attention Program in Cuba.

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