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ISSN 2174-0798 (Print)
Organo oficial de la Asociación Latinoamericana de Odontopediatría (ALOP)

2016, Number 2

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Rev Odotopediatr Latinoam 2016; 6 (2)

Dental treatment for Möebius Syndrome

Stabile-Del Vecchio RM, Morales-Chávez MC

Language: Spanish
References: 18
Page: 118-125
PDF size: 634.93 Kb.


ABSTRACT

The Moebius syndrome is a congenital disorder characterized by a paralysis of the cranial pairs, due to an atrophy of their nuclei. The facial nerve and the abducens nerve are the most affected, causing facial paralysis and limitations of the ocular movement. Other cranial nerves are also affected, which consequence is dental and skeletal anomalies. At the same time, it can be associated to malformations of upper and lower extremities, such as webbed fingers and toes and club foot. Its etiology is still unknown, but is related to a vascular problem that affects the development of the nuclei of the cranial pairs. The objective of this research is to describe the characteristics of the Moebius Syndrome, and report 3 clinical case studies that attended a dental consultation.


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