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Revista Médica Sinergia

2020, Number 05

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Revista Médica Sinergia 2020; 5 (05)

Opsoclonus–myoclonus syndrome

Delgado CLG, Benavides VJD, Marín RGJ

Language: Spanish
References: 19
Page: 420-420
PDF size: 155.63 Kb.


ABSTRACT

The opsoclonus-myoclonus syndrome is a rare medical condition associated with an autounmmune etiology, it can be paraneoplasic, parainfectios or idiopatic. The patients present with truncal and limb ataxia, falls, opsocolunus and myoclonus. Also they could present a certain degree of encephalopathy, cerebelar damage signs and sleep disturbances. In the case of the pediatric population an evaluation for neuroblastoma must be done; in adults presenting with encephalopathy a complete evaluation must be done looking an underlying neoplasia. The acute neurological symtomps can be controlled with immunotherapy and there have been a partial response to the antitumoral medication, but the long term outcome is characterized for the presence of neuropsicological deficit.


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