medigraphic.com
ISSN 0035-0052 (Print)

2020, Number 2

<< Back Next >>

Rev Mex Pediatr 2020; 87 (2)

Endocardial pacemaker in a premature infant with AV block and situs inversus totalis

Sánchez-Escobedo Y, De la Fuente-Macip C, Aquino-Bruno H, Añas-Méndez ML, Bozada-Nolasco KI, Enríquez-Silverio A, Rojel-Martínez U

Language: Spanish
References: 18
Page: 74-78
PDF size: 377.03 Kb.


ABSTRACT

Objective: We report the case of a premature newborn with congenital atrioventricular block (CAVB) and with situs inversus totalis (SIT), in whom a single-chamber endocardial pacemaker was implanted. Clinical case: Two-day-old female who was born at 35 weeks gestation and with low birth-weight. A 12-lead electrocardiogram showed a ventricular rate of 68 bpm, negative P waves in D1 and aVL and positive in aVR, with atrioventricular block 2x1. Sequential segmental analysis determined situs inversus, while a thoracic-abdominal CT scan confirmed SIT. Because data on low cardiac output were observed in the first 48 hours, and after ruling out causes of BCVB, it was decided to implant a single-chamber pacemaker endocardially. The patient evolved without complications. Conclusion: SIT is a condition that can be associated with BCVB; pacemaker implantation, even in premature infants, can improve the prognosis for these patients.


REFERENCES

  1. Cortés-Ramírez RM, Cortés de la-Torre JM, Cortés de la-Torre R, Reyes-Méndez BJ, Salazar-de Santiago RA, Carrillo Aguilar SI et al. Bloqueo AV completo congénito. Revisión y presentación de un caso. Rev Mex Cardiol. 2013; 24(3): 144-146.

  2. Li X, Huang X, Lu H. Two case reports of neonatal autoantibody-associated congenital heart block. Medicine (Baltimore). 2018; 97(45): e13185.

  3. Icardo JM, García Rincón JM, Ros MA. Congenital heart disease, heterotaxia and laterality. Rev Esp Cardiol. 2002; 55(9): 962-974.

  4. Urquia-Osorio HO, Discua-Flores LJ, Valenzuela-Castillo R. Situs inversus totalis y cardiopatía congénita: diagnóstico casual en un lactante con neumonía. CIMEL. 2010; 15(2): 85-88.

  5. Taketazu M, Lougheed J, Yoo SJ, Lim JS, Hornberger LK. Spectrum of cardiovascular disease, accuracy of diagnosis, and outcome in fetal heterotaxy syndrome. Am J Cardiol. 2006; 97(5): 720-724.

  6. Aziz PF, Tanel RE, Zelster IJ, Pass RH, Wieand TS, Vetter VL et al. Congenital long QT syndrome and 2:1 atrioventricular block: An optimistic outcome in the current era. Heart Rhythm. 2010; 7(6): 781-785. doi: 10.1016/j.hrthm.2010.02.035.

  7. Baruteau AE, Pass RH, Thambo JB, Behaghel A, Le Pennec S, Perdreau E et al. Congenital and childhood atrioventricular blocks: pathophysiology and contemporary management. Eur J Pediatr. 2016; 175(9): 1235-1248. doi: 10.1007/s00431-016-2748-0.

  8. Brito-Zerón P, Izmirly PM, Ramos-Casals M, Buyon JP, Khamashta MA. The clinical spectrum of autoimmune congenital heart block. Nat Rev Rheumatol. 2015; 11(5): 301-312. doi: 10.1038/nrrheum.2015.29.

  9. McGovern E, Kelleher E, Potts JE, O’Brien J, Walsh K, Nolke L et al. Predictors of poor outcome among children with heterotaxy syndrome: a retrospective review. Open Heart. 2016; 3: e000328. doi: 10.1136/openhrt-2015-000328.

  10. Ozawa Y, Asakai H, Shiraga K, Shindo T, Hirata Y, Hirata Y et al. Cardiac rhythm disturbances in heterotaxy syndrome. Pediatr Cardiol. 2019; 40(5): 909-913. doi: 10.1007/s00246-019-02087-2.

  11. Escobar-Diaz MC, Tworetzky W, Friedman K, Lafranchi T, Fynn-Thompson F, Alexander ME et al. Perinatal outcome in fetuses with heterotaxy syndrome and atrioventricular block or bradycardia. Pediatr Cardiol. 2014; 35(6): 906-913. doi: 10.1007/s00246-014-0874-x.

  12. Cabrera OM, Alemán FAA, Benítez RDB. Implantación de marcapaso endocavitario en un niño de 2 años por fallo del sistema epicárdico. Rev Cubana Cardiol Cir Cardiovasc. 2013; 19(2): 62-65.

  13. Vos LM, Kammeraad JAE, Freund MW, Blank AC, Breur JMPJ. Long-term outcome of transvenous pacemaker implantation in infants: a retrospective cohort study. Europace. 2017; 19(4): 581-587. doi: 10.1093/europace/euw031.

  14. Konta L, Chubb MH, Bostock J, Rogers J, Rosenthal E. Twenty-seven years experience with transvenous pacemaker implantation in children weighing < 10 kg. Circ Arrhythm Electrophysiol. 2016; 9: e003422. doi: 10.1161/CIRCEP.115.003422.

  15. Nakamoto S, Fujii K, NIshino T, Satus T, Ogawa T, Kaneda T et al. Intravenous pacemaker lead implantation for a pediatric patient: A 16- year follow- up study. Journal of Arrhythmia. 2013; 29(5): 287-290.

  16. Silvetti MS, Drago F, Di-Carlo D, Placidi S, Brancaccio G, Carotti A. Cardiac pacing in paediatric patients with congenital heart defects: transvenous or epicardial? EP Europace. 2013; 15 (9): 1280-1286. doi: 10.1093/europance/eut029.

  17. Haponiuk I, Chojnicki M, Szofer-Sendrowska A, Juscinski J, Steffens M, Jaworski R et al. “Planned” permanent pacemaker implantation in one-day-old newborn after prenatal diagnosis of congenital complete atrioventricular heart block. Kardiochir Torakochirurgia Pol. 2014; 11(1): 76-78. doi: 10.5114/kitp.2014.41937.

  18. Wilhelm BJ, Thone M, El-Scheich T, Livert D, Angelico R, Osswald B. Complications and risk assessment of 25 years in pediatric pacing. Ann Thorac Surg. 2015; 100: 147-153. doi: https://doi.org/10.1016/j.athoracsur.2014.12.098.




2020     |     www.medigraphic.com