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Antes Revista del Instituto Nacional de Enfermedades Respiratorias

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2020, Number 2

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Neumol Cir Torax 2020; 79 (2)

Thoracic surgery in a patient with osteogenesis imperfecta

Leyva-Moraga E, Ibarra-Celaya JM, Leyva-Moraga F, Hurtado-Soto LA, Castillo-Ortega G, García-Ballesteros L, Leyva-Moraga F

Language: Spanish
References: 13
Page: 94-96
PDF size: 624.87 Kb.


ABSTRACT

Introduction: Osteogenesis imperfecta is a group of heterogenous abnormalities of the collagen synthesis, characterized by multiple fractures and deformities. Thoracic surgery in patients with osteogenesis imperfecta is not common. Clinical case: We present a case of a 30 years old male with a previous diagnosis of osteogenesis imperfecta who was referred to our center for presenting a loculated empyema on his right hemithorax. A right posterolateral thoracotomy was performed. In the middle of the surgery we visualized an anatomical abnormality that coincides with an accessory fissure of the superior lobe. Conclusion: Osteogenesis imperfecta is a rare clinical entity, however the surgeon must take into consideration the physiopathological implications during the surgery.


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