Arias GA, Ramírez SK

Language: Spanish
References: 24
Page: 31-38
PDF size: 230.34 Kb.

ABSTRACT

Arrhythmogenic right ventricular cardiomyopathy is a hereditary cardiomyopathy characterized by progressive loss of myocardium and replacement with fibroadipose tissue, predominantly in the right ventricle. Here we present the case of a 42 years old male patient with a previous history of syncope who was admitted in the hospital due to right heart failure with ejection fraction of 5%. Afterwards, we discuss the most recent advances in the physiopathogenesis of this disease, the clinical and electrocardiographic manifestation, and the anatomopathological aspects of the diagnosis. The treatment and management of the disease are out of reach from this study.

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