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Revista Médica Sinergia

2020, Number 11

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Revista Médica Sinergia 2020; 5 (11)

Prune Belly syndrome

Arias VR, Herrera WG, Lobo PT

Language: Spanish
References: 20
Page: 1-9
PDF size: 171.05 Kb.


ABSTRACT

Prune Belly syndrome or Eagle-Barrett syndrome is a rare congenital disorder, with unknown etiology, characterized by the clinical triad of abdominal wall musculature hypoplasia, cryptorchidism and urinary tract malformations. Clinical presentation is variable, depending on the severity of urinary tract malformations and renal compromise. Diagnosis is usually through prenatal echography or evident at birth. Treatment of Prune Belly syndrome is primarily conservative, and surgical management depends upon the severity of symptoms, ranging from modest to more extensive procedures.


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