Valdés-Pineda, Samantha; Ramírez-Anguiano, Jaqueline; Enríquez-Figueroa, Lorena; Esquinca-González, Alexia

Language: Spanish
References: 7
Page: 181-185
PDF size: 214.38 Kb.

ABSTRACT

Background: Cholesteatoma is a cystic structure with the presence of keratin-producing squamous epithelium, which replaces the normal mucosa in the middle ear; its etiology is multifactorial, it is classified as congenital or acquired. Definitive treatment is surgical and aims to eradicate the disease. Patients with progeroid syndrome have an increased risk of presenting alterations in the middle ear such as cholesteatoma; hypohidrotic ectodermal dysplasia causes glandular disorders that increases the frequency of chronic infections at nasal and otic level.
Clinic case:A 24-year-old female patient with cholesteatoma with right mastoidectomy autocavity with a history of progeroid syndrome, probable Wermer syndrome and hypohidrotic ectodermal dysplasia, managed with conservative treatment, without complications after 10 years of follow-up.
Conclusions: Cholesteatoma of middle ear is an infrequent disease that, despite of its benign histology, may cause severe complications; thus, treatment is surgical, and its aim is to eradicate the disease.

REFERENCES

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