Morales LMJ, Vargas HMP, Miranda SL

Language: Spanish
References: 15
Page: 1-11
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ABSTRACT

Clear cell sarcoma of the kidney is the second most frequent malignant kidney tumor in pediatric age, after Wilms tumor. It is a neoplasm of difficult diagnosis, with a nonspecific clinical presentation such as palpable abdominal mass, abdominal pain, and hypertension and hematuria. The imaging characteristics of this lesion are nonspecific, so its diagnosis is made through the pathological study of the tumor. Its importance revolves around the diagnostic difficulty, since this tumor presents great histological variability and few adequate immunohistochemical markers. Treatment includes neoadjuvant and post-surgical chemotherapy, with a prognosis that improves if the disease is diagnosed early.

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