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2020, Number 6

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Rev Mex Pediatr 2020; 87 (6)

Gastroduodenal trichobezoar or Rapunzel syndrome in a 6-year-old girl

Arenas-Rojas AM, Villamizar-Durán LI

Language: Spanish
References: 23
Page: 236-239
PDF size: 223.22 Kb.


ABSTRACT

Objective: To describe the case of a school-age patient with Rapunzel syndrome, given that it is a rare condition in this age-group and that there are few cases reported in Latin America. Case report: A 6-year-old female patient with a history of trichotillomania and trichophagia, with recurrent abdominal pain and malnutrition. The physical examination revealed alopecia and indurated and well-defined abdominal mass. By ultrasound and endoscopy a large gastroduodenal trichobezoar was found, so the diagnosis of Rapunzel syndrome was made. The trichobezoar was removed by laparotomy, and the patient was subsequently maintained with psychiatric treatment. Conclusions: Rapunzel syndrome is uncommon in pediatric age, requiring a high index of suspicion for its diagnosis. Management must be multidisciplinary.


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