Ávila LVH, Saeb LM

Language: Spanish
References: 14
Page: 24-27
PDF size: 219.94 Kb.

ABSTRACT

Muir-Torre syndrome is a rare genodermatosis, characterized by the presence of sebaceous neoplasms and/or multiple keratoacantome associated with the presence of an internal malignant neoplasm. We report a 55-year-old male with a history of colon adenocarcinoma and he also presented a tumor on the left gluteal region with a three-month evolution, to which an excisional biopsy was performed. Sebaceous adenocarcinoma, presenting lack of expression of MSH2 and MSH6, confirming Muir-Torre syndrome.

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