Jiménez Y Felipe, Joel Higinio; Castillo- Aldaco, Juan D; Rascón- Alcántar A

Language: Spanish
References: 16
Page: 102-107
PDF size: 312.99 Kb.

ABSTRACT

Tracheal Agenesis (AT) is a congenital condition and in most of the cases reported die immediately after birth. It is do- cumented that some children with non-complete AT are treated with tracheostomy. The objective is a description of a newborn with tracheal agenesis with an extrauterine survival of 6 hours, an autopsy was performed confirming the diag- nosis of tracheal agenesis, a literature review is made. Clinical case present a male neonate, product of the second pregnancy with pelvic presentation born by caesarean section, which develops respiratory failure and generalized cyanosis, performing a tracheostomy, is sent to the Emergency Department of our Unit. Upon admission he presented irreversible cardio-respiratory arrest to resuscitation maneuvers. Autopsy revealed AT. Few are the cases that have survived tracheal agenesis, such as those referred to by Sankara y collaborators (1983), where only the upper part of the trachea was missing and a tracheostomy was achieved at the immediate end. Some current embryological concepts are reviewed, as well as the classification suggested by Faro and collaborators (1973). The treatment of Fonkalsrud y collaborators (1963) is also mentioned for difficult cases. There is currently no definitive treatment for this congenital condition.

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