2012, Number S5
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ABSTRACTIntroduction: chronic Cor Pulmonale is a syndrome characterized by pulmonary hypertension and failure of right heart secondary to a variety of primary diseases of the pleura, lungs, chest wall and pulmonary circulation. His relationship with the final phase of infiltrative lung disease is well described in the literature.
Objectives: to describe an unusual case of chronic cor pulmonale pulmonary fibrosis in a young patient with no history of progressive dyspnea.
Case: young woman of 35 who entered the hospital with dyspnea, abdominal pain and severe lower limb edema. On physical examination was found also heart murmur, jugular venous distension and hepatomegaly failure. CT was performed transthoracic lung which was diagnosed right heart failure and severe pulmonary fibrosis.
Conclusions: radiological and echocardiographic study demonstrated the presence of chronic Cor Pulmonale due to acute interstitial pneumonitis.
World Health Organization. Chronic Cor pulmonale. A report of the expert committee. Circulation. 1963;2:594-8.
Gómez-Doblas JJ, Velasco JL, Alarcón PL, Montiel AT. Cor pulmonale. Etiopatogenia. Proceso diagnóstico. Criterios pronósticos. Tratamiento. Medicine. 2005;9:2873-8.
Llorente JL. Enfermedad pulmonar intersticial difusa. Medicine. 2002; 8(79): 4223-9.
Ryerson CJ, Donesky D, Pantilat SZ, Collard HR. Dyspnea in idiopathic pulmonary fibrosis: a systematic review. J Pain Symptom Manage. 2012, Apr;43(4):771-82.
Richeldi L. Assessing the treatment effect from multiple trials in idiopathic pulmonary fibrosis. Eur Respir Rev. 2012, Jun 1;21(124):147-51.
Faner R, Rojas M, Macnee W, Agusti A. Abnormal Lung Aging in Chronic Obstructive Pulmonary Disease and Idiopathic Pulmonary Fibrosis. Am J Respir Crit Care Med. 2012, May 10.
Kim DS. Acute exacerbation of idiopathic pulmonary fibrosis. Clin Chest Med. 2012, Mar;33(1):59-68.
Chong SG, O'Brien A, Casserly B. Interstitial pneumonitis with bronchiolitis: presentation of a case and review of the literature. Arch Bronconeumol. 2012, Jul;48(7):262-3.
Andersen CU, Mellemkjær S, Hilberg O, Nielsen-Kudsk JE, Simonsen U, Bendstrup E. Pulmonary hypertension in interstitial lung disease: prevalence, prognosis and 6 min walk test. Respir Med. 2012, Jun;106(6):875-82.
Wuyts WA, Thomeer M, Demedts MG, Verleden GM. New idiopathic pulmonary fibrosis guidelines: some unresolved questions. Am J Respir Crit Care Med. 2012, Mar 1;185(5):588.
Margaritopoulos GA, Romagnoli M, Poletti V, Siafakas NM, Wells AU, Antoniou KM. Recent advances in the pathogenesis and clinical evaluation of pulmonary fibrosis. Eur Respir Rev. 2012, Mar 1;21(123):48-56.
Jawad H, Chung JH, Lynch DA, Newell JD Jr. Radiological approach to interstitial lung disease: a guide for the nonradiologist. Clin Chest Med. 2012, Mar;33(1):11- 26.
Behr J. Approach to the diagnosis of interstitial lung disease. Clin Chest Med. 2012, Mar;33(1):1-10.