Ginecología y Obstetricia de México

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>Journals >Ginecología y Obstetricia de México >Year 2015, Issue 03

Ávila-Vergara MA, León-Álvarez DA, López-Villegas MN, Quintero-Medrano SM, Angulo-Bueno GF, Vadillo-Ortega F
Mayer-Rokitansky-Küster-Hauser Syndrome: Two cases report
Ginecol Obstet Mex 2015; 83 (03)

Language: Espańol
References: 13
Page: 199-205
PDF: 348.71 Kb.

Full text


Agenesia of the Müllerian ducts is a low-frequency congenital disease but with devastating effects on women’s reproductive health. In this paper we present two cases of women affected by Mayer-Rokitansky- Küster-Hauser syndrome (MRKH). First case was a 17-year-old woman with aplasia of the upper vagina and absence of uterus. No other defects were found and was classified as type 1-MRKH. Second case was 18-year-old woman with absence of uterus, escoliosis and polycystic ovary syndrome, classified as type II-MRKH. Patients were seen at the Hospital with primary amenorrhea and fully developed secondary sexual characteristics. A clinical follow-up protocol, including the use of high-resolution image studies was used for diagnosis. Diagnostic procedures and current medical approaches to the treatment of MRKH are discussed, including psychological advisory, surgical procedures and new tissue-engineering techniques.

Key words: Primary amenorrhea, uterine-vaginal aplasia, Mayer- Rokitansky-Küster-Hauser syndrome.


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>Journals >Ginecología y Obstetricia de México >Year 2015, Issue 03

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