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>Journals >Cirujano General >Year 2007, Issue 1

Cerdán PR, Bernal JJ, Cantín BS, Barranco DJI, Borlán AS, Serrablo RA, Esarte MJM
Digestive hemorrhage due to stromal tumor located in the jejunum in a patient with neurofibromatosis
Cir Gen 2007; 29 (1)

Language: Español
References: 19
Page: 54-57
PDF: 4. Kb.

Full text


Objective: To report the case of a female patient with neurofibromatosis and gastrointestinal hemorrhage induced by jejunal stromal tumor.
Setting: Third level health care hospital.
Case description: Gastrointestinal stromal tumors (GIST) are originated in the mesenquimal tissue of the gastrointestinal wall. They are usually located in the stomach, and the jejunum is the second most frequent location. We report a case of a 57-year-old woman, with neurofibromatosis type 1 and admitted to the hospital because of an acute gastrointestinal bleeding. Laparotomy revealed a proximal jejunal tumor that was classified as GIST. We analyze the ultrastructural characteristics of these tumors, their forms of presentation, and their diagnostic difficulties when lesions are located in the small bowel.
Conclusion: Association between GIST and neurofibromatosis is an inusual finding, frequently producing symptoms that require surgical treatment.

Key words: GIST, neurofibromatosis type 1, stromal tumors, gastrointestinal hemorrhage.


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>Journals >Cirujano General >Year 2007, Issue 1

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