Acta Ortopédica Mexicana

Ruiz-Mejía O, Pimentel-Rangel J, Oribio-Gallegos JA, Valle LG, Esquivel-Vallejo A, Vega-España EA
Orthopedic management of localized linear scleroderma in children: a case report
Acta Ortop Mex 2019; 33 (4)

Language: Español
References: 15
Page: 261-264
PDF: 141.41 Kb.

[Fulltext - PDF]


Introduction: Localized scleroderma is the most common form of sclerosis in children; it has an incidence of 2.7 per 100,000 inhabitants, with a predilection for the Caucasian and female races of 2.4 to 4.1 per male. The common denominator is the connective tissue-level condition, causing a variety of clinical presentation ranging from localized sclerotic circumscribed plaques affecting the skin, to deeper conditions that attack muscle and bone tissue, leaving aesthetic consequences and/or disabling deformities in the patient. Objective: Case presentation and surgical management. The data presented were obtained from the physical and electronic clinical record, direct interview with patients and family members and monitoring and evaluation of radiographic studies, from January 2012 to November 2017. Discussion: Surgical treatment is indicated when deformities and contractures condition incapacity in the patient. The best results will be obtained once the disease has stopped progressing.

Key words: Localized scleroderma, morphea, orthopedic sequelae, children, orthopedic management.


  1. Rebollo DN, Gutiérrez MD, Fonte AV, Vega ME. Morfea una revisión. Dermatología CMQ. 2007; 5(4): 224-33.

  2. Fett N, Werth VP. Update on morphea. part II. Outcome measures and treatment. J Am Acad Dermatol. 2011; 64(2): 231-42.

  3. Zancanaro PC, Isaac AR, Garcia LT, Costa IM. Esclerodermia localizada na criansa: aspectos clínicos, diagnosticos e terapêuticos. An Bras Dermatol. 2009; 84(2): 161-72.

  4. Vancheeswaran R, Black CM, David J, Hasson N, Harper J. Childhood onset scleroderma; it is different from adult onset diseases. Arthritis and Rheumatism. 1996; 39(6): 1041-49.

  5. Zulian F, Vallongo C, Woo P, Russo R, Ruperto N, Harper J, et al. Localized scleroderma in chilhood. is not just a skin disease. Arthritis Rheum. 2005; 52(9): 2873-81.

  6. Zulian F, Woo P, Athreya BH, Laxer RM, Medsger TA Jr, Lehman TJ, et al. The Pediatric Rheumatology European Society/American College of Rheumatology/European league against rheumatism provisional: classification criteria for juvenile systemic sclerosis. Arthritis and Rheumatism. Arthritis Rheum. 2007; 57(2): 203-12.

  7. Zulian F. Systemic sclerosis and localized sclerodermain childhood. Reum Dis Clin North Am. 2008; 34(8): 239-51.

  8. Vera LOL. Esclerosis sistémica. Med Int Mex. 2006; 22(3): 231-45.

  9. Martínez EV, Medina CD, Cantú CPP. Esclerosis sistémica progresiva. Rev Cent Dermatol Pascua. 2005; 14(1):9-18.

  10. Bielsa MI. Actualización en la clasificación y el tratamiento de la esclerodermia localizada. Actas Dermo-Sifiliográficas. 2013; 104(8): 654-66.

  11. Siham Z, Poisson LM, Karima B, Fatima L, Abdellatif EF. Linear scleroderma and foot deformity in children: case report. Open J Clin Med Case Report. 2017; 3(12): 1-7.

  12. Kathryn S. Pediatric scleroderma: systemic and localized forms. Pediatr Clin North Am. 2012; 59(2): 381-405.

  13. Pastor OJ, Calcedo AA, Paricio TJ, Santos SL, Fernández FA, Ferriol CM. Esclerodermia lineal: lesion en golpe de sable. An Esp Pediatr. 1998; 49: 499-502.

  14. Buckley SL, Skinner S, James P, Ashley RK. Focal scleroderma in children on orthopaedic perspective. J Pediatr Orthop. 1993; 13(6): 784-90.

  15. Kato H, Morita A. A surgical approach for stable lesions of linear scleroderma. Kaohsiung J Med Sci. 2010; 26: 621-23.