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Table 1: Skin involvement status by category of vasculitis and disease. |
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CHCC2012 vasculitis category, name |
Skin involvement status |
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Cutaneous component of systemic vasculitis |
Limited or dominant skin variant |
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Large vessel vasculitis |
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Takayasu arteritis |
No |
No |
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Giant cell arteritis |
Rare |
No |
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Medium vessel vasculitis |
Yes |
Yes |
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Polyarteritis nodosa |
Yes |
Yes |
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Kawasaki disease |
No |
No |
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Small vessel vasculitis |
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Microscopic polyangiitis |
Yes |
Yes |
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Granulomatosis with polyangiitis |
Yes |
Yes |
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Eosinophilic granulomatosis with polyangiitis |
Yes |
Yes |
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Anti-glomerular basement membrane disease |
No |
No |
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Cryoglobulinemic vasculitis |
Yes |
Yes |
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IgA vasculitis (Henoch-Schönlein) |
Yes |
Yes |
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Urticarial hypocomplementemic vasculitis (anti-C1q vasculitis) |
Yes |
Yes |
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Variable vessel vasculitis |
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Behçet’s disease |
Yes |
Yes |
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Cogan’s syndrome |
Rare |
No |
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Vasculitis associated with systemic disease |
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SLE, rheumatoid vasculitis, sarcoid vasculitis, etc. |
Yes |
Yes |
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Vasculitis associated with probable etiology |
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Drugs, infections, sepsis, autoimmune diseases, etc. |
Yes |
Yes |
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Cutaneous SOV (not included in CHCC2012) |
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IgM/IgG vasculitis |
No (not observed yet) |
Yes (as SOV) |
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Nodular vasculitis (erythema induratum of Bazin) |
No |
Yes (as SOV) |
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Nodular vasculitis (Bazin’s indurated erythema) |
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Erythema elevatum et diutinum |
No |
Yes (as SOV) |
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Hypergammaglobulinemic macular vasculitis |
No |
Yes (as SOV) |
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Normocomplementemic urticarial vasculitis |
No |
Yes (as SOV) |
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CHCC2012 = 2012 revised International Chapel Hill Consensus Conference Nomenclature of Vasculitides; SLE = systemic lupus erythematosus; SOV = single-organ vasculitis. |
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