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>Revistas >Cirugía y Cirujanos >Año 2008, No. 1


Orozco-Gómez LP, Castellanos-Pérez BCG, Moguel-Ancheita S, Lambarri-Arroyo A
Estudio de las distrofias vitreorretinianas en población mexicana
Cir Cir 2008; 76 (1)

Idioma: Español
Referencias bibliográficas: 45
Paginas: 13-21
Archivo PDF: 192.91 Kb.


Texto completo




RESUMEN

Objetivo: Determinar la incidencia de las variedades de las distrofias vitreorretinianas en población mexicana ya que no existen reportes de la misma en la literatura.
Material y métodos: estudio retrospectivo, observacional, descriptivo y transversal con revisión de expedientes de pacientes con enfermedades retinianas de 1991 al 2006, para determinar la incidencia de distrofias vitreorretinianas.
Resultados: Fueron analizados 36,300 expedientes del Servicio de Retina revisados de enero de 1991 a diciembre de 2006 en el Centro Médico Nacional 20 de Noviembre, hospital de tercer nivel de referencia nacional de los pacientes derechohabientes del ISSSTE, en quienes se encontró una incidencia de 0.008 % para distrofia exudativa familiar, 0.008 % para retinosquisis juvenil ligada al cromosoma X, 0.005 % para la enfermedad de Wagner y 0.005 % para la enfermedad de Goldmann Favré. Presentamos casos representativos de los mismos.
Conclusiones: Las distrofias vitreorretinianas son enfermedades raras, de difícil diagnóstico, pero aunque su incidencia es baja, la tórpida evolución hacia la ceguera obliga a identificar los signos precoces para un tratamiento más oportuno.


Palabras clave: Distrofias vitreorretinianas, retinosquisis juvenil, vitreorretinopatía exudativa familiar, enfermedad de Goldmann-Favré, síndrome de Wagner-Stickler.


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>Revistas >Cirugía y Cirujanos >Año2008, No. 1
 

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