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>Journals >Cirugía y Cirujanos >Year 2008, Issue 1


Orozco-Gómez LP, Castellanos-Pérez BCG, Moguel-Ancheita S, Lambarri-Arroyo A
Study of vitreoretinal dystrophies in a Mexican population
Cir Cir 2008; 76 (1)

Language: Español
References: 45
Page: 13-21
PDF: 192.91 Kb.

[Full text - PDF]

ABSTRACT

Background: We undertook this study to demonstrate the incidence of vitreoretinal dystrophies in a Mexican population.
Methods: This was a retrospective, observational, descriptive and transversal study. We analyzed the files of patients treated at the Retina Department in a medical center for state employees (ISSSTE) from January 1991 to December 2006 to obtain the incidence of vitreoretinal dystrophies.
Results: We studied 36,300 patient files. We found an incidence of 0.008 % for familial exudative vitreoretinal dystrophy, 0.008 % for X-linked juvenile retinoschisis, 0.005 % for Wagner disease and 0.005 % for Goldmann-Favre disease. We present here a representative case of each type of dystrophy.
Conclusions: Vitreoretinal dystrophies are uncommon diseases and are difficult to diagnose. Even though they have a low incidence, the poor evolution to blindness requires identification of early signs in order to offer timely and opportune treatment.


Key words: Vitreoretinal dystrophies, Goldman-Favre disease, X-linked juvenile retinoschisis, familial exudative vitreoretinal dystrophy, Wagner-Stickler syndrome.


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>Journals >Cirugía y Cirujanos >Year 2008, Issue 1
 

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