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2021, Number 3

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Dermatología Cosmética, Médica y Quirúrgica 2021; 19 (3)

Behçet’s disease. A case report with benign intracranial hypertension without cerebral venous thrombosis and empty sella syndrome as a manifestation of neuro-Behçet

Reyes WDA, Melo AR, Tinajero NL

Language: Spanish
References: 13
Page: 256-259
PDF size: 319.92 Kb.


ABSTRACT

Behçet’s disease (BD) is a multisystemic, multifactorial vasculitis associated with the major histocompatibility complex (MHC) of chromosome 6 and HLA-B*51. The main clinical features are: recurrent oral ulcers, genital ulcers and eye lesions. The diagnosis of BD is made with the International Criteria for Behçet’s Disease (ICBD) 2014. Treatment will depend on the affected organ/ system.
We present a 27-year-old female with a history of bacterial pharyngotonsillitis with oral ulcers, arthritis, and erythema nodosum. She started with frontal headache, tunnel vision, oral and genital ulcers. Diagnosis of Behçet’s disease with non-parenchymal neurological involvement was made, initiating induction of remission with cyclophosphamide, with adequate clinical response.
BD is a chronic, relapsing disease, with high morbidity and mortality, frequently diagnosed late due to the need to exclude differential diagnoses and the lack of specific markers of the disease. Multidisciplinary management is required for the prevention- treatment of its complications.


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