Uribe-Franco RC, Milán-Salvatierra AI

Language: Spanish
References: 15
Page: 181-188
PDF size: 290.38 Kb.

ABSTRACT

Background: Hairy cell leukemia, along with diffuse splenic lymphoma, are mature B-cell lymphoid disorders, the peculiar characteristic of which are the cytoplasmic processes that give the appearance of a hairy cell. It is 4 to 5 times more frequent in men than in women and represents 2% of all leukemias, the course of this disease is indolent, asymptomatic cytopenias are usually found, on some occasions there are constitutional symptoms, abdominal distention due to organomegaly.
Clinical case: A 37-year-old female patient in who hairy cell leukemia was diagnosed after the study due to having fever of unknown origin.
Conclusions: Purine analogs with responses of up to 90-100% are recommended as first-line. Not all newly diagnosed patients are eligible for treatment, symptomatic disease is only monitored.

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