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2021, Number 2

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Cuba y Salud 2021; 16 (2)

Dermatofibrosarcoma Protuberans: Presentación De Caso

Tamayo CAM, Cuastumal FDK, Pérez CKY, Arteaga HE

Language: Spanish
References: 13
Page: 150-155
PDF size: 1568.42 Kb.


ABSTRACT

Objective: To emphasize the therapeutic and reconstructive options available.
Method: We present a 59-year-old patient with a tumor lesion in the frontal region of 11 years of evolution, with 6 reoperations due to several recurrences, admitted with a report of benign pathology, resected with wide safety margins and closure with lateral advancement flap and complementary total skin graft. The biopsy of the surgical specimen demonstrated the existence of protuberant dermatofibrosarcoma.
Discussion: When a malignant lesion is suspected, the safety margins must be taken into account, which in this case range from 1 to 5 cm. The safest surgeries are wide local excision with tumor-free margins and Mohs micrographic surgery. The closure of the exposed area will be decided according to age, location and availability of techniques. When there are doubts about incomplete resection of the lesion, the use of an autologous skin graft is preferred.
Conclusions: this malignant tumor, although infrequent, can occur in plastic surgery patients who seek its cure with the least possible deforming sequela. It is the responsibility of the reconstructive surgeon to have knowledge of this entity and its therapeutic options, to offer the best aesthetic result with the lowest rate of recurrence.


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