2023, Number 04
PDF size: 376.78 Kb.
ABSTRACTBackground: Klippel Trenaunay syndrome is a rare congenital disease characterized by capillary and venous malformations, limb overgrowth and in some cases lymphatic malformations. Sufferers have an increased risk of hemorrhage and thromboembolism.
Clinical cases: Three primigravid patients diagnosed with Klippel Trenaunay syndrome with pregnancy complications that were terminated by cesarean section with the birth of their healthy, full-term children in all cases.
Conclusions: Women with Klippel-Trenaunay syndrome and pregnancy are at significant risk for aggravation of their symptoms, hemorrhage during birth, and thromboembolic events, even after birth. Individualized, multidisciplinary care will help mitigate associated complications and achieve optimal outcomes.
Bates S M, Greer I A, Mideeldorp S, Veenstra D L, Prabulos AM, Vandvik P O. Venous thromboembolism, thrombophilia,antithrombotic therapy and pregnancy. Antithrombotictherapy and prevention of trombosis, 9th ed: AmericanCollege of Chest Physicians evidence-based clinical practiceguidelines. Chest 2012; 14 (2 suppl) e 691S-765S.doi:10.1378/chest.11-2300.