Osuna-Camacho V, Cossío-Lara GM, González-Acosta FC, Espinoza-Beltrán JM, Morales-Sanchez FF, Rochín Teran JL, Beltrán Ontiveros SA, López-López K

Language: Spanish
References: 8
Page: 66-73
PDF size: 238.03 Kb.

ABSTRACT

Moebius syndrome is a congenital neurological pathology characterized by unilateral or bilateral hypoplasia or agenesis of the abducens (VI) and facial (VII) nerves, leading to facial paralysis and limitation of ocular abduction by the lateral rectus muscle. Patients with this síndrome mainly manifest facial expressionlessness and lack of outward eye movement. A clinical case of a 6-year-old male patient with a diagnosis of Möebius síndrome was detected, his clinical detection was made after manifesting facial paralysis and limitation in the abduction of the gaze since birth, whitout previous imaging studies that confirmed said diagnosis by image method. In this report, the agenesis of cranial nerves VI and VII is evidenced by the nuclear magnetic resonance imaging method using the FIESTA (Fast Imaging Employing Steady-State –Acquisition). Knowledge about Moebius syndrome guides us to clinical suspicion and an accurate diagnosis based on physical examination and the implementation of imaging services such as nuclear magnetic resonance using the FIESTA sequence, wich allows the patient to be given timely treatment for prevent clinical complications, as well as improve their quality of life..

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